Long-Term Prophylaxis Therapy in Patients with Hereditary Angioedema with C1 Inhibitor Deficiency

Hereditary angioedema with C1 inhibitor (C1-INH) deficiency (C1-INH-HAE) is a rare condition that may have a profound effect on patients' lives, both physically and emotionally.1, 2 Swelling can occur in the abdomen, face, throat, genitalia, or extremities and may cause pain and disability. Abdominal swelling can cause severe pain and potentially intestinal obstruction, incapacitating the patient during the attack. Swelling of the extremities can impede patients from walking or using their hands, and swelling with airway involvement is potentially life-threatening.

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